ENDOCRINE DISORDERS

 

DR SIMON ATTARD MONTALTO

 

 

GROWTH

 

Short stature

 

endocrine:

constitutional delay

GH deficiency

hypothyroidism

cushing syndrome

non endocrine:

syndromes

chromosomal

orthopaedic

low birth weight

systemic disease

hereditary disease

psychological/deprivation

 

Tall stature

 

endocrine:

constitutional tall stature

GH excess

hyperthyroidism

androgen excess

precocious puberty

congenital adrenal hyperplasia (CAH)

non endocrine:

syndromes

chromosomal (Klinefelter)

orthopaedic

other (Soto, Marfan)

hereditary disease (homocystinuria)

 

PUBERTY

 

Delay

 

endocrine:

constitutional delay

gonadotrophic deficiency

hypopituitarism

non endocrine: syndromes

chromosomal

congenital abnormalities

systemic disease

trauma

neoplasia

psychological/deprivation

 

Precocious

 

endocrine:

idiopathic/physiological

gonadotrophin excess

excess steroids

androgen excess

CAH

non endocrine:

syndromes

congenital abnormalities/malformations

SOL

 

THYROID

 

Deficiency

primary:

congenital

autoimmune (Hashimoto)

thyroiditis

infection

secondary:

iodine deficiency

pituitary deficiency (TSH)

surgery

neoplasia, radiotherapy

 

Excess:

autoimmune (Grave’s)

solitary nodule

exogenous T4

 

ADRENALS

 

Deficiency

primary:

autoimmune

haemorrhage

infection

iatrogenic

secondary:

pituitary deficiency (ACTH)

post excess steroid therapy

trauma, surgery

neoplasia, radiotherapy

 

Excess (glucocorticoids)

Cushing disease

Cushing syndrome - iatrogenic, adrenal tumour, other tumour

 

Excess (mineralocorticoids)

CAH

 

DIABETES MELLITUS

 

HLA b8, B15, DR3, DR4

islet cell antibodies

autoimmune process

trigger (?viral)

associated with cystic fibrosis, pancreatitis

 

Clinical

polyuria, polydipsia, weight loss, lassitude, dehydration

diabetic ketoacidosis (DKA) - 25%

 

Diagnosis

hyperglycaemia + glycosuria +/- DKA

DKA

§         correct dehydration

§         correct electrolytes (esp K+)

§         correct acidosis

§         correct hyperglycaemia

 

DIABETES INSIPIDUS

 

Central

ADH deficiency

congenital adenoma

infection (meningitis)

iatrogenic (surgery)

trauma

local infiltration / neoplasia

congenital syndromes

 

Nephrogenic

X-linked disorder

tubular resistance to ADH

renal abnormalities

sickle cell disease